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KMID : 0361720140250020105
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Korean Journal of perinatology
2014 Volume.25 No. 2 p.105 ~ p.109
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A Case of Diffuse Cutaneous Mastocytosis in a Newborn
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Park Mi-Na
Kim Geun-A
Chey Myoung-Jae
Shim Gyu-Hong
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Abstract
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Diffuse cutaneous mastocytosis (DCM) is a rare variant of mast cell disease with widespread erythema and is clinically apparent in early infancy. We report the case of a 1-day-old female neonate who presented with diffuse flush, pruritus, and extensive blistering. DCM was diagnosed by immunohistochemical staining with anti-CD117, which revealed mast cell infiltration. DCM is a severe and heterogeneous cutaneous disease, and is associated with mast cell mediator-related symptoms and risk of anaphylactic shock. We describe this case and provide the first literature review of neonatal onset DCM in Korea.
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KEYWORD
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Cutaneous mastocytosis, Diffuse cutaneous mastocytosis, Newborn
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